Imaging findings in a case with cholesteatoma in complete aural atresia

We report a case of cholesteatoma in congenital aural atresia in which preoperative imaging analysis provided useful information. A 30-year-old man with total aural atresia had had ear symptoms on his right side for 10 years. Evaluation by computerized tomography and magnetic resonance imaging suggested that the mass in the atretic external auditory canal and the anterior part of the mastoid was cholesteatoma and that the mass in the posterior part of the mastoid was inflammatory granulation tissue and chronic osteomyelitis. Three-dimensional fluid-attenuated inversion recovery images showed increased signals in the labyrinth. The extent of the cholesteatoma revealed during surgery was consistent with the preoperative image findings. Imaging analysis provides useful information for management of congenital aural atresia, and combined examination with computerized tomography and magnetic resonance imaging could be beneficial for preoperative evaluation of state of ears in cases of congenital aural atresia.