TY - JOUR
T1 - Mitral valve surgery in a patient with spinal progressive muscular atrophy
T2 - Report of a case
AU - Takami, Yoshiyuki
AU - Ina, Hiroshi
AU - Terasawa, Akihiro
AU - Nakao, Masahide
N1 - Funding Information:
This work was supported by Research Project CEZ: AV0Z4055905, the Grant Agency of the Czech Republic (Grant No. 303/01/0690) and by the Ministry of Education of the Czech Republic (Grant No. LN00A032 and Grant No. MSM 113100001).
PY - 2003
Y1 - 2003
N2 - We describe our experience in treating a 69-year-old man with spinal progressive muscular atrophy (SPMA), who underwent a mitral valve replacement. He was admitted for dyspnea, and surgery was indicated for severe mitral insufficiency associated with inferior myocardial infarction. He had been aware of muscle weakness and received a diagnosis of SPMA 18 years previously. Worsening muscle atrophy had led to the need for him to use a wheelchair in his daily life. A preoperative examination revealed markedly reduced pulmonary function (% volume capacity = 44.8%). Because of an acute exacerbation of heart failure, the patient underwent an urgent mitral valve replacement with a 27-mm pericardial bioprosthesis. Although it took 42 h to wean him from the mechanical ventilation and he suffered from pulmonary atelectasis after extubation, he was discharged from our hospital in a wheelchair 16 days after surgery. Respiratory management with bilevel positive airway pressure was thus found to be quite useful for patients with neuromuscular disease.
AB - We describe our experience in treating a 69-year-old man with spinal progressive muscular atrophy (SPMA), who underwent a mitral valve replacement. He was admitted for dyspnea, and surgery was indicated for severe mitral insufficiency associated with inferior myocardial infarction. He had been aware of muscle weakness and received a diagnosis of SPMA 18 years previously. Worsening muscle atrophy had led to the need for him to use a wheelchair in his daily life. A preoperative examination revealed markedly reduced pulmonary function (% volume capacity = 44.8%). Because of an acute exacerbation of heart failure, the patient underwent an urgent mitral valve replacement with a 27-mm pericardial bioprosthesis. Although it took 42 h to wean him from the mechanical ventilation and he suffered from pulmonary atelectasis after extubation, he was discharged from our hospital in a wheelchair 16 days after surgery. Respiratory management with bilevel positive airway pressure was thus found to be quite useful for patients with neuromuscular disease.
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U2 - 10.1007/s10595-002-2517-9
DO - 10.1007/s10595-002-2517-9
M3 - Article
C2 - 14506997
AN - SCOPUS:0037676155
SN - 0941-1291
VL - 33
SP - 521
EP - 524
JO - Surgery Today
JF - Surgery Today
IS - 7
ER -