Staged management of pseudoexstrophy with omphalocele and wide pubic diastasis

Pseudoexstrophy is a rare, mild exstrophy variant characterized by the major musculoskeletal defects of the exstrophy complex without associated defects of the urinary system. The authors present a case of pseudoexstrophy with a small omphalocele and wide pubic diastasis (greater than 4 cm). Only three cases of pseudoexstrophy with omphalocele have previously been described worldwide, and this is the first reported case with wide pubic diastasis. Successful two-stage surgery consisting of omphalocele repair in the neonatal period and abdominoplasty with iliac osteotomy after the age of 6 months is described.