Transvenous Embolization for carotid-cavernous fistula in a patient with vascular type of ehlers-danlos syndrome-direct superior ophthalmic vein approach

Case report

Teppei Tanaka, Motoharu Hayakawa, Akiyo Sadato, Kazuhide Adachi, Takeya Watabe, Shingo Maeda, Masahiro Ohmura, Yuichi Hirose

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

The vascular type of Ehlers-Danlos syndrome (vEDS) is an autosomal dominant hereditary disease characterized by connective tissue fragility throughout the body, including the arteries, viscera, and gastrointestinal tract. We report a case in which we performed transvenous embolization (TVE) via direct superior ophthalmic vein (SOV) approach to treat a direct carotid-cavernous fistula (CCF) in a patient with Ehlers-Danlos syndrome (EDS). The patient was a 37-year-old woman who developed tinnitus in her left ear and a headache during examination in the outpatient clinic of another hospital in order to make a definitive diagnosis of vEDS, and she was referred to our hospital and examined. Based on the results of all of the studies she was diagnosed with a CCF. Conservative treatment was attempted, but was not very effective. Because of progressing aphasia, TVE was performed via the SOV direct cut. There were no intraoperative or postoperative complications. It has been reported that cerebral angiography is generally contraindi-cated in vEDS and that the morbimortality associated with endovascular treatment is very high. When performing treatment it is necessary to be sufficiently aware of the risks it entails.

Original languageEnglish
Pages (from-to)155-160
Number of pages6
JournalNeurologia medico-chirurgica
Volume54
Issue number2
DOIs
Publication statusPublished - 20-02-2014

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Ehlers-Danlos Syndrome
Fistula
Veins
Hospital Outpatient Clinics
Cerebral Angiography
Inborn Genetic Diseases
Viscera
Tinnitus
Aphasia
Intraoperative Complications
Connective Tissue
Ear
Headache
Gastrointestinal Tract
Arteries
Therapeutics

All Science Journal Classification (ASJC) codes

  • Surgery
  • Clinical Neurology

Cite this

Tanaka, Teppei ; Hayakawa, Motoharu ; Sadato, Akiyo ; Adachi, Kazuhide ; Watabe, Takeya ; Maeda, Shingo ; Ohmura, Masahiro ; Hirose, Yuichi. / Transvenous Embolization for carotid-cavernous fistula in a patient with vascular type of ehlers-danlos syndrome-direct superior ophthalmic vein approach : Case report. In: Neurologia medico-chirurgica. 2014 ; Vol. 54, No. 2. pp. 155-160.
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Transvenous Embolization for carotid-cavernous fistula in a patient with vascular type of ehlers-danlos syndrome-direct superior ophthalmic vein approach : Case report. / Tanaka, Teppei; Hayakawa, Motoharu; Sadato, Akiyo; Adachi, Kazuhide; Watabe, Takeya; Maeda, Shingo; Ohmura, Masahiro; Hirose, Yuichi.

In: Neurologia medico-chirurgica, Vol. 54, No. 2, 20.02.2014, p. 155-160.

Research output: Contribution to journalArticle

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