A case of juvenile dermatomyositis with Sjögren's syndrome

We report here a 7-year-old patient with juvenile dermatomyositis (JDM) associated with Sjögren's syndrome. When the patient was one year old, her mother detected skin eruptions on her legs. Her mother also noted muscle weakness characterized by progressive slowing of her walking speed and frequent stumbling. At the age of two, she was diagnosed with JDM and treated with oral steroids. At the age of three, she presented to our hospital with facial erythema, heliotrope erythema, Gottron's sign, and muscle weakness. Sjögren's syndrome was dignosed when she was 4 years old. Her facial erythema improved remarkably by protection from sunlight with sunscreen cream. Skin and muscle manifestations have not recurred, but she occasionally experiences parotid gland swelling.