A pediatric patient with classical citrullinemia who underwent living-related partial liver transplantation

Kyoko Ban, Naruji Sugiyama, Kohachiro Sugiyama, Yoshiro Wada, Tatsuya Suzuki, Takashi Hashimoto, Keiko Kobayashi

研究成果: Article査読

28 被引用数 (Scopus)

抄録

Patients with inborn errors of metabolism undergo liver transplantation, but the effect of transplanting the liver of healthy carriers of these conditions has not been fully clarified. A 6-year-old girl with classical citrullinemia, who repeatedly suffered from hyperammonemia, underwent living-related liver transplantation by using a segment of the liver of her mother, who was a heterozygote carrier for classical citrullinemia. Hyperammonemia alleviated in the patient after the transplantation, thereby dramatically improving her quality of life. Although the levels of plasma and urinary citrulline remained high postoperatively, there was no marked difference in the level of plasma citrulline up to 1 month after surgery when compared with that of previously reported orthotopic liver transplantation cases with classical citrullinemia.

本文言語English
ページ(範囲)1495-1497
ページ数3
ジャーナルTransplantation
71
10
DOI
出版ステータスPublished - 27-05-2001
外部発表はい

All Science Journal Classification (ASJC) codes

  • 移植

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