Pulmonary Veno-Occlusive Disease (PVOD) Associated with Connective Tissue Disease

Hidekata Yasuoka, Masataka Kuwana

研究成果: Article査読

抄録

Pulmonary arterial hypertension (PAH) associated with connective tissue disease (CTD) has a worse prognosis than that of idiopathic PAH, even when drugs for PAH treatment, such as vasodilators, are used. In cases of CTD-PAH, if pulmonary veins or venules are also affected, the condition is termed pulmonary veno-occlusive disease (PVOD). PVOD is thought to worsen the prognosis of CTD-PAH. Although surgical biopsy is required for a definitive diagnosis of PVOD. findings of chest computed tomography (CT) or the response to PAH drugs may facilitate diagnosis. There is no effective treatment for PVOD except lung transplantation. However, immunosuppressive therapy may be one treatment choice for PVOD associated with CTD. Treatment strategies should be "tailor-made" for each patient since CTD patients usually have multiple-organ involvement.

本文言語English
ページ(範囲)270-278
ページ数9
ジャーナルJapanese Journal of Chest Diseases
73
3
出版ステータスPublished - 03-2014
外部発表はい

All Science Journal Classification (ASJC) codes

  • 呼吸器内科

フィンガープリント

「Pulmonary Veno-Occlusive Disease (PVOD) Associated with Connective Tissue Disease」の研究トピックを掘り下げます。これらがまとまってユニークなフィンガープリントを構成します。

引用スタイル