Pseudoexstrophy is a rare, mild exstrophy variant characterized by the major musculoskeletal defects of the exstrophy complex without associated defects of the urinary system. The authors present a case of pseudoexstrophy with a small omphalocele and wide pubic diastasis (greater than 4 cm). Only three cases of pseudoexstrophy with omphalocele have previously been described worldwide, and this is the first reported case with wide pubic diastasis. Successful two-stage surgery consisting of omphalocele repair in the neonatal period and abdominoplasty with iliac osteotomy after the age of 6 months is described.
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